Primary adenocarcinoma of the duodenum associated with cutaneous neurofibromatosis (von Recklinghausen's disease).

Introduction The association of neurofibromatosis with malignant tumours of the neural crest is well documented. Neurofibromatosis may also be associated with other malignant tumours such as carcinoid of the ampulla of Vater (Barber, 1976), adenocarcinoma of the pancreas (Kellar and Logan, 1977), adenocarcinoma of the colon (Jenkins and Gill, 1972), Wilms' tumour (Stay and Vauter, 1977), rhabdomyosarcoma (McKeen and Bodurtha, 1978) and leukaemia (Bader and Miller, 1978). The authors wish to report the association of primary adenocarcinoma of the duodenum in a young man suffering from cutaneous neurofibromatosis.